Vol. 2, Issue 4, Part B (2016)

Abstract: Parry-Romberg Syndrome (PRS) or idiopathic hemifacial atrophy is a rare developmental craniofacial syndrome. It is characterized by slowly progressive atrophy of one side of the face, primarily involving the skin, fat and connective tissue. It is an acquired condition of unknown aetiology presenting usually in childhood or adolescence, with gradual progression over several years. A multidisciplinary approach is effective in the management of this disorder. We present a case report of PRS in a15 year old girl with the review of aetiology, clinical features and treatment of PRS. The diagnosis was established mainly based on clinical and radiological findings. Clinicians must be aware of PRS to identify the invalidating disorder.