Vol. 5, Issue 3, Part E (2019)

Abstract: Angelman syndrome (AS) is a genetic disorder characterized by intellectual disability, movement or balance disorders, specific abnormal behaviors, and severe speech and language limitations. Many patients with AS may have difficulty with medical evaluations and may require general anesthetics for seemingly innocuous procedures including the dental care. At the same time AS poses significant challenges for the anaesthetist due to sensitivity to anesthetic agents and the craniofacial abnormalities. This paper describes the use of deep sedation for dental treatment provided for a 7-year-old patient with AS.