Objective: To analyze the literature on the considerations in the dental office in the management of the hemophiliac patient, particularly the etiology, clinical characteristics, diagnosis, treatment and dental management.

Methodology: In order to carry out this literature review, an electronic search was necessary using PUBMED and Google Scholar with the words "Hemophilia AND dentistry" "etiology, clinical and dental characteristics, diagnosis and treatment" and "coagulation factors".

Results: Hemophilia is due to an alteration in one of the genes that determine the way in which the organism produces coagulation factor VIII or IX. It occurs in 1 in 10,000 male births. It manifests as excessive bleeding in the joints, pain and edema, ecchymosis, urinary tract and digestive tract bleeding. It results in prolonged bleeding from wounds, dental extractions and surgery. The diagnosis of hemophilia is made by taking a blood sample and measuring the degree of factor activity. The main treatment for severe hemophilia is to receive specific clotting factor replacement. During the consultation, a detailed medical history should be taken and comprehensive clinical examinations should be ordered appropriately. The patient should provide the following information: type and severity of his hemophilia, medication ingest, whether he requires pre-treatment with factor concentrate, or an antifibrinolytic agent.

Conclusion: Hemophilia is an X-linked recessive inherited disorder. It belongs to the group of inherited disorders caused by deficiency of one or more clotting factors. Practice guidelines are needed to improve the diagnostic process, improve the quality of dental care.