Vol. 8, Issue 2, Part F (2022)

Abstract: Congenital insensitivity to pain with anhidrosis (CIPA) is a rare disease characterized by recurrent fever episodes, mental retardation of different intensity, anhidrosis, little or no perspiration and congenital insensitivity to pain. Oral self-mutilation is also a characteristic sign. In this article, we present a case who showed these clinical characteristics and was treated with a dental device to prevent the patient from injuring his tongue. Neuropathies treatment is a great challenge for medical teams. Pediatric dentist should be a part of these teams because of the oral implications that may appear. The recognition and awareness of this rare clinical condition may be helpful in reaching a correct diagnosis and offering symptomatic treatment, to avoid potential tissue damage at an earlier stage of the disease.